TY - JOUR
T1 - Inflammatory myopathies and systemic disorders
T2 - A review of immunopathogenetic mechanisms and clinical features
AU - Mantegazza, Renato
AU - Bernasconi, Pia
AU - Confalonieri, Paolo
AU - Cornelio, Ferdinando
PY - 1997
Y1 - 1997
N2 - The inflammatory myopathies are a heterogeneous group of muscle diseases characterized by muscle degeneration mediated by inflammatory processes. They may be idiopathic, as in polymyositis, dermatomyositis and inclusion body myositis, or associated with systemic disorders such as malignancies, overlap syndromes, and retroviral infection. The pathogenesis of each disease is discussed together with more recent molecular and cellular immunology findings. Salient diagnostic, clinical and pharmacological features are also reviewed.
AB - The inflammatory myopathies are a heterogeneous group of muscle diseases characterized by muscle degeneration mediated by inflammatory processes. They may be idiopathic, as in polymyositis, dermatomyositis and inclusion body myositis, or associated with systemic disorders such as malignancies, overlap syndromes, and retroviral infection. The pathogenesis of each disease is discussed together with more recent molecular and cellular immunology findings. Salient diagnostic, clinical and pharmacological features are also reviewed.
KW - Autoimmunity
KW - Collagen vascular diseases
KW - Inflammatory myopathies
KW - Malignancies
KW - Muscle
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U2 - 10.1007/s004150050087
DO - 10.1007/s004150050087
M3 - Article
C2 - 9178151
AN - SCOPUS:0030976227
SN - 0340-5354
VL - 244
SP - 277
EP - 287
JO - Journal of Neurology
JF - Journal of Neurology
IS - 5
ER -