How should i treat a left persistent superior vena cava with unroofed coronary sinus associated with severe stenosis and regurgitation of aortic homograft placed in the tricuspid position?

Valeria Pergola, Giovanni Di Salvo, Mohammed Al-Admawi, Bahaa Fadel, Mansour Al-Jufan, Massimo Chessa, Jonathan McGuinness

Research output: Contribution to journalArticlepeer-review

Abstract

BACKGROUND: A 21-year-old man with a history of atrial septal defect (ASD) and ventricular septal defect (VSD) repair and tricuspid valve (TV) replacement with size 22 mm aortic homograft presented complaining of severe shortness of breath. Clubbing and cyanosis of the fingers were noted. SpO2 on room air was 80-84%. INVESTIGATION: Physical examination, electrocardiogram, chest X-ray, transthoracic echocardiography, CT scan, right cardiac catheterisation. DIAGNOSIS: Persistent left superior vena cava draining into the left atrium through an unroofed coronary sinus, severe stenosis and regurgitation of homograft in the tricuspid position. MANAGEMENT: Percutaneous closure of left superior vena cava draining into the left atrium through an unroofed coronary sinus with concomitant percutaneous implantation of a Melody valve in the tricuspid position.

Original languageEnglish
Pages (from-to)e1491-e1494
JournalEuroIntervention
Volume13
Issue number12
DOIs
Publication statusPublished - Dec 1 2017

Keywords

  • Ebsteinoid tricuspid valve
  • Persistent left superior vena cava
  • Unroofed coronary sinus

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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