TY - JOUR
T1 - How should i treat a left persistent superior vena cava with unroofed coronary sinus associated with severe stenosis and regurgitation of aortic homograft placed in the tricuspid position?
AU - Pergola, Valeria
AU - Di Salvo, Giovanni
AU - Al-Admawi, Mohammed
AU - Fadel, Bahaa
AU - Al-Jufan, Mansour
AU - Chessa, Massimo
AU - McGuinness, Jonathan
PY - 2017/12/1
Y1 - 2017/12/1
N2 - BACKGROUND: A 21-year-old man with a history of atrial septal defect (ASD) and ventricular septal defect (VSD) repair and tricuspid valve (TV) replacement with size 22 mm aortic homograft presented complaining of severe shortness of breath. Clubbing and cyanosis of the fingers were noted. SpO2 on room air was 80-84%. INVESTIGATION: Physical examination, electrocardiogram, chest X-ray, transthoracic echocardiography, CT scan, right cardiac catheterisation. DIAGNOSIS: Persistent left superior vena cava draining into the left atrium through an unroofed coronary sinus, severe stenosis and regurgitation of homograft in the tricuspid position. MANAGEMENT: Percutaneous closure of left superior vena cava draining into the left atrium through an unroofed coronary sinus with concomitant percutaneous implantation of a Melody valve in the tricuspid position.
AB - BACKGROUND: A 21-year-old man with a history of atrial septal defect (ASD) and ventricular septal defect (VSD) repair and tricuspid valve (TV) replacement with size 22 mm aortic homograft presented complaining of severe shortness of breath. Clubbing and cyanosis of the fingers were noted. SpO2 on room air was 80-84%. INVESTIGATION: Physical examination, electrocardiogram, chest X-ray, transthoracic echocardiography, CT scan, right cardiac catheterisation. DIAGNOSIS: Persistent left superior vena cava draining into the left atrium through an unroofed coronary sinus, severe stenosis and regurgitation of homograft in the tricuspid position. MANAGEMENT: Percutaneous closure of left superior vena cava draining into the left atrium through an unroofed coronary sinus with concomitant percutaneous implantation of a Melody valve in the tricuspid position.
KW - Ebsteinoid tricuspid valve
KW - Persistent left superior vena cava
KW - Unroofed coronary sinus
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U2 - 10.4244/EIJ-D-16-00050
DO - 10.4244/EIJ-D-16-00050
M3 - Article
AN - SCOPUS:85039791267
SN - 1774-024X
VL - 13
SP - e1491-e1494
JO - EuroIntervention
JF - EuroIntervention
IS - 12
ER -