A Rare Variant of Hypogenetic Lung Syndrome Mimicking Scimitar Vein

Tommaso D'Angelo, Alfredo Blandino, Michele B Saitta, Salvatore Agati, Placido Romeo, Silvio Mazziotti

Research output: Contribution to journalArticlepeer-review


Hypogenetic lung syndrome, also known as scimitar syndrome, is a rare and well-known congenital condition that includes hypoplastic right pulmonary artery and lung, right displacement of the heart, anomalous systemic arterial supply to the lung, and a characteristically curved anomalous right pulmonary vein draining into the inferior vena cava. In exceptional cases, the anomalous pulmonary vein may drain into left atrium. We here report a case of a 17-year-old girl with a rare variant of hypogenetic lung syndrome diagnosed by means of multimodality imaging and treated with percutaneous occlusion of the aortopulmonary collateral.

Original languageEnglish
Pages (from-to)e173-e176
JournalAnnals of Thoracic Surgery
Issue number3
Publication statusPublished - Sept 2021


  • Abnormalities, Multiple/diagnosis
  • Adolescent
  • Diagnosis, Differential
  • Female
  • Heart Atria/abnormalities
  • Humans
  • Pulmonary Veins/abnormalities
  • Scimitar Syndrome/classification
  • Vena Cava, Inferior/abnormalities


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